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Abstract

Objectives: To study the frequency and spectrum of congenital cyanotic heartdisease among patients attending pediatric cardiology department for suspectedcardiac problem.Methodology: This was an observational study, conducted in PediatricCardiology Department Lady Reading Hospital Peshawar, from 1 September2012 to 31 August 2013.Every patient with suspected cardiac problem wassubjected to echocardiographic study to know frequency and spectrum ofcongenital cyanotic heart disease in these patient.Results: Total number of patient studied with congenital heart disease (CHD) was2342. Of them 434(18.53%) were found to have cyanotic congenital heartdisease (CCHD). Of these CCHD patients males were 262(60.36%). Mean agewas 34.42±30.34 months (from 1 day to 18 years). Tetrology of fallot (TOF)patients were 205(47.23%) which forms 8.8% of total CHD. 0f these TOF patients09 were already corrected. Transposition of great arteries (TGA) was found in83(19.12%). Ebstein with cyanosis were found in 12(2.76%) patients. DoubleOutlet Right Ventricle (DORV) was found in 38 (8.75%). Total anomalouspulmonary venous drainage (TAPVD) patients were 27(6.22%). Of thesesupracardiac TAPVD were 15(3.45%), Cardiac TAPVD were 7(1.61%) andInfracardiac TAPVD were 5(1.15%). Pulmonary atresia with intact pulmonaryseptum was found in 15(3.4%).Single ventricle was found in 21(4.84%) patients.Eisenmenger syndrome was found in 11(2.6%). Hypoplastic left heart was foundin 14 (3.22%) and 8(1.84%) having truncusarteriosus.Conclusion: About 18% of CHD in our population comprises of CCHD. TOF is themajor CCHD in our population.Key Words: Cyanotic Congenital Heart Disease (CCHD), Tetrology of Fallot(TOF),Transposition of Great Arteries(TGA)