DefinePK

Abstract

Pulmonary agenesis is a very rare condition with poor prognosis. Although the condition is a congenital malformations, delayed presentation is also seen. A female neonate with left pulmonary agenesis presented to us with severe respiratory distress. She was initially misdiagnosed as a case diaphragmatic hernia at another hospital and referred to us for further management. Clinical examination and further investigations confirmed the diagnosis of left pulmonary agenesis. The child improved on medical management and is asymptomatic up to 6 months of follow-up.