DefinePK

Abstract

We report a 58 yr old lady, who had right temple swelling for 2 years, which on excision biopsy showed features of vasculitis. During the Rheumatology review, Clinical evaluation didn’t reveal any features suggestive of Giant cell arteritis and inflammatory markers were normal. She had localised granulomatous changes without giant cells and pathologist gave the opinion as Kimura’s disease. It has been described in East Asia especially in Japan as Juvenile Giant cell vasculitis (also known as Kimura’s disease (KD). It was reported by Kimura et al. as chronic inflammatory disorder of unknown aetiology with granulomatous changes mimicking vasculitis but no giant cells. It is very rare in Caucasians and early diagnosis will result in appropriate treatment and sparing the immunomodulatory treatment. This case is presented to increase awareness of KD and to highlight the features which may aid the diagnosis.