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Abstract

Cerebrofacial arteriovenous metameric syndrome (CAMS) is a recent classification of vascular malformations that encompasses a spectrum of phenotypic expression involving arteriovenous malformations (AVMs) of the cerebral, orbital and facial region. Recognizing the CAMS is important for diagnosing other AVMs along the same metameric level. We present a case with intraparenchymal AVM and maxillofacial AVM without optic nerve involvement, characteristics of CAMS 2. The diagnosis of intracranial and facial AVM was made by magnetic resonance imaging of the brain and confirmed with digital subtraction angiography.