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Abstract

Introduction: Congenital cystic lesions of lung present an interesting spectrum of pathology in the paediatric population. Congenital lobar emphysema (CLE), congenital pulmonary airway malformation (CPAM), Sequestration, intrapulmonary cystic teratomas are rare conditions found in children.
Aim and objective: To evaluate the clinical presentation, investigation modalities, operative management, pathology, outcome (morbidity and mortality) and follow-up of congenital cystic lesions of the lung.
Material and Methods: This was a prospective observation study conducted in the Department of Paediatric Surgery Centre and P.G. Institute. All the cases of congenital cystic lung lesion operated at this institute during the period of August 2018 to January 2021 were studied. A total of 22 patients presented solitary lesions: CCAM, CLE, PS, BC were screeded. The Methods used to detect and confirm CCLL were as chest X-ray, CT scans, and others.
Results: In the present study we included 22 cases of congenital cystic lung lesions & observed for a period of August 2018 to January 2021. In our study the malformations included congenital cystic lesion was distributed in 4 types in which most common was Congenital lobar overinflation (CLO) with 45% of incidence, Congenital pulmonary airway malformation (CPAM) with 32%, Bronchogenic cyst with 18% and Pulmonary sequestration with 5%. Maximum patients were in the age group 0 to 3 months 59% respectively. Slight male preponderance was seen in this study. All patients have undergone surgical excision in terms of lobectomy or excision of the lesion. Post-operative histopathology confirmed the diagnosis.
Conclusion: Congenital cystic lung lesions are typically detected prenatally and managed through observation or surgery, depending on severity. Early diagnosis and treatment generally lead to good outcomes, with ongoing research aimed at improving detection and long-term care